XPHEN TYR Tyrosidon is a phenylalanine- and tyrosine-free powdered mixture of other essential and non-essential amino acids. Suitable for infants, children and adults for the dietary management of tyrosinaemia where plasma methionine levels are normal.
XPHEN TYR Tyrosidon is a phenylalanine- and tyrosine-free powdered mixture of other essential and non-essential amino acids.
Important notice:
For enteral use only. Not for parenteral use.
Must be used under medical supervision.
Not suitable as a sole source of nutrition.
Suitable from birth.
Only to be used by individuals with proven tyrosinaemia where plasma methionine levels are normal.
Precautions: This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the isoleucine, leucine, valine and general nutrition requirements of the patient.
Suggested intake: The quantity of feed and the dilution should be determined by a clinician or dietitian only, and is dependent on the age, bodyweight and medical condition of the patient.
Recommended feed concentration:
1 to 20 (e.g. 1g powder plus 20ml water) = 370 mOsmol/kg H2O
Paste the prescribed quantity of powder with a small
amount of water before gradual dilution to final volume.
This dilution is a guideline only. Can be taken as a more concentrated drink or paste, but additional water or diluted drinks should be offered at the same time.
Unopened: Store in a cool, dry place.
Opened: Use within 4 weeks. Always replace container lid after use.
Prepared feed: Refrigerate and consume within 24 hrs
Suitable for infants, children and adults for the dietary management of tyrosinaemia where plasma methionine levels are normal.
L-lysine, L-glutamate, L-leucine, L-proline, L-arginine, L-valine, L-isoleucine, glycine, L-aspartic acid, L-threonine, L-serine, dried glucose syrup, L-alanine, L-histidine, L-cystine, L-tryptophan, L-methionine, L-glutamine, L-glutamic acid, tricalcium phosphate, taurine, L-carnitine.
| Nutritional information per | 100 g | ||
|---|---|---|---|
| ENERGY | 1386 kJ / 326 kcal | ||
| FAT of which | 0 g | ||
| -Saturates | - | ||
| -Monounsaturates | - | ||
| -Polyunsaturates | - | ||
| -Linoleic acid (LA) | - | ||
| -Alpha linolenic acid (ALA) | - | ||
| -Arachidonic acid (ARA) | - | ||
| -Docosahexaenoic acid (DHA) | - | ||
| CARBOHYDRATE of which | 4.5 g | ||
| Sugars | 0.4 g | ||
| FIBRE | 0 g | ||
| PROTEIN EQUIVALENT of which | 77 g | ||
| L-Alanine | 4.1 g | ||
| L-Arginine | 7.16 g | ||
| L-Aspartic acid | 5.98 g | ||
| L-Cystine | 2.66 g | ||
| L-Glutamic acid | 8.04 g | ||
| L-Glutamine | 0.81 g | ||
| Glycine | 6.4 g | ||
| L-Histidine | 4.09 g | ||
| L-Isoleucine | 6.4 g | ||
| L-Leucine | 10.97 g | ||
| L-Lysine | 7.46 g | ||
| L-Methionine | 1.75 g | ||
| L-Phenylalanine | -* | ||
| L-Proline | 7.77 g | ||
| L-Serine | 4.79 g | ||
| L-Threonine | 5.38 g | ||
| L-Tryptophan | 2.15 g | ||
| L-Tyrosine | -* | ||
| L-Valine | 6.99 g | ||
| SALT | <0.05 g | ||
| VITAMINS | |||
| Vitamin A | - | ||
| Vitamin D | - | ||
| Vitamin E | - | ||
| Vitamin E | - | ||
| Vitamin C | - | ||
| Vitamin K | - | ||
| Thiamin | - | ||
| Riboflavin | - | ||
| Niacin | - | ||
| Niacin | - | ||
| Vitamin B6 | - | ||
| Folic acid | - | ||
| Folate | - | ||
| Vitamin B12 | - | ||
| Biotin | - | ||
| Pantothenic acid | - | ||
| MINERALS & TRACE ELEMENTS | |||
| Sodium | <20 mg | ||
| Potassium | - | ||
| Chlorine | - | ||
| Calcium | 126 mg | ||
| Phosphorous | 65 mg | ||
| Magnesium | - | ||
| Iron | - | ||
| Copper | - | ||
| Zinc | - | ||
| Manganese | - | ||
| Iodine | - | ||
| Molybdenum | - | ||
| Selenium | - | ||
| Chromium | - | ||
| OTHERS | |||
| L-Carnitine | 0.06 g | ||
| Choline | - | ||
| Inositol | - | ||
| Taurine | 0.12 g | ||
| Osmolality | 370 mOsmol/kg H₂O** | ||
-Each level scoop contains 5g of powder.
*Nil added
** At the recommended dilution of 1 to 20 (i.e. 1g MSUD AID III plus 20ml water)
Disclaimer
XPHEN TYR Tyrosidon is food for medical use and should be used under medical supervision. Always follow the advice of your treating dietitian before making any changes to the diet. Consult with your treating dietitian whether XPHEN TYR Tyrosidon is suitable for you or your child.
These products are Foods for Special Medical Purposes and should be used under medical supervision.
This section is meant for people with a metabolic disorder, their parents/carers, or Healthcare Professionals.
Do you belong to one of these groups?
