If you're just starting or restarting your PKU diet, it's good to review your protein sources. Your protein substitute is essential to give your body the right nutrients.

Your protein substitute: the basis of your diet

Your PKU protein substitute is your main source of protein, providing your body with essential amino acids with no or very little phenylalanine. Think of it as a tailor-made shake especially for people with PKU.

Why are protein substitutes necessary?

PKU protein substitutes:

• Contain all essential amino acids, but little or no phenylalanine.
• Are often enriched with tyrosine, an amino acid that PKU patients cannot produce properly themselves.
• Come in a variety of shapes and flavours, so you can choose an option that suits your preference.
• Some contain glycomacropeptide (GMP), a natural protein from cheese whey that is low in phenylalanine, which often provides a better taste.
• Can be used in foods and beverages, making them easier to fit into your daily diet.

Your protein substitute should be used as directed by your treating dietitian. This forms the basis of your daily protein intake, so don't skip it!

Different types of PKU protein substitutes

There are several types of protein substitutes available, so you can choose an option that suits your lifestyle in consultation with your dietitian:

• Powders: Mix with water or another protein-free liquid in a shaker.
• Liquids: Ready-to-drink drinks, ideal for on the go.
• Tablets: Handy if you don't want a shake

Discuss with your dietitian which form best suits your needs. The available products and brands vary by country, so make sure you are well informed.

Factors to consider

• Calories: Protein substitutes are available with different calorie contents. Discuss with your doctor or dietician which one suits you best.
• Volume: Many protein substitutes can be mixed with different amounts of water, so you get a thicker or a more diluted drink.
• Taste: there are protein substitutes in different flavors. Try out which one you like best!

Need help?

Would you like more information or change your diet? Then contact your treating dietitian.

Starting your diet (again) is a valuable step for your health. It can be challenging, but remember: you're not alone, and your body will thank you for it!